Gender | Male, 4 (66.6Â %) |
Female, 2 (33.3Â %) | |
Diagnosis | Definite, 3 (50Â %) |
Progressive, 3 (50Â %) | |
Age at presentation (Mean ± SD) | 47.17 ± 10.17 (38–65) years |
Age at onset (Mean ± SD) | 46.37 ± 9.98 (37.5–64) years |
Duration of illness (Mean ± SD) | 11.3 ± 6.6 (6.0–24) months |
Onset pattern | Bulbar, 4 (66.6Â %) |
Limb, 2 (33.3Â %) |